{"id":94,"date":"2006-08-16T21:16:12","date_gmt":"2006-08-16T19:16:12","guid":{"rendered":"http:\/\/146.107.134.84\/wordpress\/index.php\/2006\/08\/16\/german-human-geneticists-and-nbia\/"},"modified":"2006-08-21T10:37:18","modified_gmt":"2006-08-21T08:37:18","slug":"german-human-geneticists-and-nbia","status":"publish","type":"post","link":"https:\/\/www.wjst.de\/blog\/sciencesurf\/2006\/08\/german-human-geneticists-and-nbia\/","title":{"rendered":"Geneticists and NBIA-PKAN"},"content":{"rendered":"<p>Geneticists continue to publish about &#8220;Hallervorden-Spatz&#8221; or &#8220;former Hallervorden-Spatz&#8221; syndrome.<\/p>\n<p><a href=\"http:\/\/www.hoffnungsbaum.de\/text5krankheitsbild.html\">The German<\/a> NBIA patient group advocates for many years that these names should be abandoned (the <a href=\"http:\/\/www.nbiadisorders.org\/\">American<\/a> patient group even formally changed its name 2003). NBIA is a rare inherited neurological movement disorder characterized by the progressive degeneration of the nervous system; NBIA means &#8220;neurodegeneration with brain iron accumulation&#8221;. Another frequently used disease synonym is pantothenate kinase-associated neurodegeneration (PKAN).<\/p>\n<p>The clinical syndrome has been described by the neurologist Julius Hallervorden and the neuropathologist Hugo Spatz. Robert Jay Lifton does not h>ave any material about Hallervorden and Spatz in &#8220;<a href=\"http:\/\/www.amazon.de\/gp\/product\/0465049052\/302-2838443-9924862?v=glance&#038;n=52044011&#038;s=gateway&#038;v=glance\">The Nazi Doctors: Medical Killing and the Psychology of Genocide<\/a><a href=\"http:\/\/www.amazon.de\/gp\/product\/0465049052\/302-2838443-9924862?v=glance&#038;n=52044011&#038;s=gateway&#038;v=glance\">&#8220;<\/a> but Ernst Klee in &#8220;<a href=\"http:\/\/www.amazon.de\/gp\/product\/3596149061\/302-2838443-9924862?v=glance&#038;n=299956&#038;s=gateway&#038;v=glance\">Auschwitz, die NS-Medizin und ihre Opfer<\/a>&#8221; and Benno M&uuml;ller-Hill in  &#8220;<a href=\"http:\/\/www.amazon.de\/gp\/product\/0879695315\/303-8369168-1169068?v=glance&#038;n=52044011\">Murderous science<\/a>&#8221; mentions both. Professor Hugo Spatz (1888-1969) was docent in Munich 1923, director of Kaiser-Wilhelm-Institut Berlin 1937-1945 and director of Max-Planck-Institut f&uuml;r Hirnforschung Gie\u00dfen 1948-1957. Professor Julius Hallervorden (1882-1965) was department head at Kaiser-Wilhelm-Institut Berlin 1938-1945 and at MPI for Brain Research from 1948 on.<\/p>\n<p>The former director of Max-Planck association Professor Hubertus Markl mentioned their involvement in Nazi euthanasia in his <a href=\"http:\/\/www.mpg.de\/pdf\/redenPraesidenten\/001014mahnmalMarkl.pdf\">lecture on Oct 14, 2000<\/a> at MDC in Berlin-Buch (own translation): &#8220;Recent research showed that brains of hundreds of euthasia victims killed between 1939 and 1944 in Brandenburg-G\u00f6rden, were mis-used for research purposes. In a single case Julius Hallervorden was present in person, while children were killed in G\u00f6rden and brains consecutively analysed in his laboratory&#8230; As a biologist it remains for me to declare that this is an eternal dishonor for German bioscience.&#8221;<\/p>\n<p><!---XXX 15944911 ---><\/p>\n\n<p>&nbsp;<\/p>\n<div class=\"bottom-note\">\n  <span class=\"mod1\">CC-BY-NC Science Surf , accessed 09.04.2026<\/span>\n <\/div>","protected":false},"excerpt":{"rendered":"<p>Geneticists continue to publish about &#8220;Hallervorden-Spatz&#8221; or &#8220;former Hallervorden-Spatz&#8221; syndrome. The German NBIA patient group advocates for many years that these names should be abandoned (the American patient group even formally changed its name 2003). NBIA is a rare inherited neurological movement disorder characterized by the progressive degeneration of the nervous system; NBIA means &#8220;neurodegeneration &hellip; <a href=\"https:\/\/www.wjst.de\/blog\/sciencesurf\/2006\/08\/german-human-geneticists-and-nbia\/\" class=\"more-link\">Continue reading <span class=\"screen-reader-text\">Geneticists and NBIA-PKAN<\/span> <span class=\"meta-nav\">&rarr;<\/span><\/a><\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[2],"tags":[3,2945,13],"class_list":["post-94","post","type-post","status-publish","format-standard","hentry","category-genetics-biology","tag-ethics-law","tag-genetics-biology","tag-history-insights"],"_links":{"self":[{"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/posts\/94","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/comments?post=94"}],"version-history":[{"count":0,"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/posts\/94\/revisions"}],"wp:attachment":[{"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/media?parent=94"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/categories?post=94"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.wjst.de\/blog\/wp-json\/wp\/v2\/tags?post=94"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}